Kidney nontumor
Primary glomerular diseases
Congenital nephrotic syndrome

Author: Nikhil Sangle, M.D. (see Authors page)

Revised: 15 September 2017, last major update April 2012

Copyright: (c) 2002-2017, PathologyOutlines.com, Inc.

PubMed Search: Congenital nephrotic syndrome [title] "loattrfree full text"[sb]

See also: Diffuse mesangial sclerosis, Finnish type
Cite this page: Sangle, N. Congenital nephrotic syndrome. PathologyOutlines.com website. http://pathologyoutlines.com/topic/kidneycongenitalnephroticsyndrome.html. Accessed October 24th, 2017.
Definition / general
  • Heterogenous conditions with nephrotic syndrome within first 3 months of life
  • Onset between 3 - 12 months is called infantile nephrotic syndrome
  • No response to steroids or immunosuppressive therapy
  • Divided into Finnish type and diffuse mesangial sclerosis but may also be a part of a more generalized syndrome or caused by a perinatal infection (Pediatr Nephrol 2009;24:2121)
Diagrams / tables

Images hosted on other servers:

Normal glomerular capillary and capillary wall

Treatment
  • Renal transplant
Differential diagnosis